Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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This is the result of a lack of migration of neuroblasts from the neural crest to the large intestine during embryonic period. The patient was asymptomatic while awaiting definitive surgical treatment. Enfermedad de Hirschsprung en hirdchsprung adulto. The principal aim of the journal is to publish original work in the broad field of Gastroenterology, as well as to provide information on the specialty and related areas that is up-to-date and relevant.

Hirschsprung’s disease HD is a malformation of the large intestine characterized by the absence of ganglion ve in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1.

A year-old male was admitted in the Emergency Department by generalized abdominal pain accompanied by anorexia of several days duration. Hirschsprung’s disease in adults: The pathologist’s report showed the existence of ulceration foci with acute inflammation in the submucosa. After that, the palpable mass disappeared, but clinical constipation persisted. A resection of distal rectal mucosa of the aganglionic segment is performed, maintaining muscular wall of this segment.

Vólvulo en adultos | HCA Healthcare

We include a review of existing literature. Therefore, the most liquid stools upstream pass around the fecal impaction and produce the reported symptom, known as fecal incontinence soiling. Biopsies of the rectum.


The treatment of choice is surgical and aganglionic segment resection and anastomosis of the healthy colonic segment to the anal canal can be performed laparoscopically. A CT scan was performed, showing a massive dilatation of sigmoid colon, which compresses liver to the right upper quadrant, stomach into the left upper quadrant and bowel loops into the right flank Figs. CT scan was performed, showing signs of peritonitis caused by dehiscence of ileum-rectal suture.

The treatment is surgical, removing the aganglionic segment and restoring continuity of digestive tract. Discussion Hirschsprung’s disease affects about 1 in 5, live births and usually presents in neonatal period.

Therefore, fecal incontinence can cause emotional disturbances to patients, with subsequent relationship problems at school and with their own families. The aganglionic segment is sectioned into the abdomen. The adults consult for a chronic constipation history, abdominal distension, use of laxatives and enemas since childhood.

You can change the settings or obtain more hirschssprung by clicking here. The age of patients ranges from 10 to 73 years old. The surgical approach will depend on length of aganglionic area, length and reversibility of colonic dilatation, and nutritional status of patient. S protein detection of neuronal cells: There was neuronal dysplasia with scarce presence of ganglion cells on both edges of resection.

Rev Col Gastroenterol, 22pp. A transition zone was appreciated in distal sigmoid colon.

Discussion Some authors have maintained that Hirschsprung’s disease in adults probably correspond to congenital cases not diagnosed previously, and consequently it is likely that, in fact, adult Hirschsprung’s disease does not really exist as an independent entity. It consists in a rear section of muscular wall of rectum starting from dentate line by transanal waywhich removes some of the top segment of internal anal sphincter, getting relief stenosis. This is an open-access article distributed under the terms of the Creative Commons Attribution License.


Enfermedad de Hirschsprung del adulto: To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. Peripheral aerial imagery was found in the dilated segment, gas-like wall, which is thickened in this segment.

Our patient had a history of long-standing bowel constipation, progressing to fecal incontinence.

Vólvulo en adultos

Plain films typically show a massive expansion of proximal colon, with a small distal segment. J Pediatr Surg ; Rev Esp Enferm Dig, 3pp.

The diagnostic is supported with studies of the barium enema, anorectal manometry and inmunohistochemestry. Abdomen was very distended and tympanic, with previous laparotomy scar, painful on palpation diffusely.

Services on Adltos Article. The authors declare that there is no conflict of interest. Then, normal colon is lowered through the aganglionic segment, making an anastomosis at level of Morgagni columns. Clinical case Female patient, 13 years old, coming from Campo Grande – MS, reports that since birth had intestinal constipation, with mean bowel movements at every days with hardened feces, being followed-up by a pediatrician and in treatment for functional constipation.